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Anti -HADHA Rabbit pAb

價(jià)格: 在線咨詢
貨號(hào):
KT011921
產(chǎn)品規(guī)格:
100 μL
Applications:
WB
Species:
MR
購(gòu)買數(shù)量:
產(chǎn)品詳情 操作說(shuō)明 注意事項(xiàng)

Product Information


Description

HADHA rabbit polyclonal antibody

Protein full name

Trifunctional enzyme subunit alpha, mitochondrial

Synonyms

Monolysocardiolipin acyltransferase, TP-alpha, HADHA

Immunogen

KLH conjugated Synthetic peptide corresponding to Mouse HADHA

Isotype

IgG

Purity

Affinity purification

Predicted MW.

83 kDa

Observed MW.

74 kDa

Uniprot ID

Q8BMS1, Q64428




Applications


Applications

Species

Dilution

Positive Sample

WB

Mouse, Rat

1: 500-1: 1000

heart, liver, kidney




Background


This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency.




Images


Picture 1.png

Western blot analysis of HADHA (GB111284) at dilution of 1: 500




Storage


Storage Store at -20 ℃ for one year. Avoid repeated freeze/ thaw cycles.
Storage Buffer PBS with 0.02% sodium azide, 100 μg/ml BSA and 50% glycerol.




NOTE:

1.This product is intended for research only.

2.This product is recommended to dilute with the Primary Antibody Dilution Buffer .


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